NZPAH Trust and Support Group

Supporting, educating and promoting awareness of PAH

Key Facts No 1

What is pulmonary hypertension?

Pulmonary hypertension (PH) is a condition which affects the lungs and heart.1 It is characterized by high blood pressure in the arteries of the lungs. There are five different types of PH which affects people in different ways, but all can lead to heart failure. The mortality rate of the more rare type of PH, pulmonary arterial hypertension (PAH), can be higher than that of certain forms of cancers. 2,3The prevalence of this rare form is estimated to be approximately 50 cases per million people.4






  1. Ruiz-Cano, M et al. Comparison of Baseline Characteristics and Survival between Patients with Idiopathic and Connective Tissue Disease-related Pulmonary Arterial Hypertension. J Heart Lung Transplant 2009,28:621-627
  2. Verdecchia, A et al.
  3. Mclaughin. W et al. ACCF/ASHA2009 expert consensus document on pulmonary hypertension. J Am CollCardol2009 28,53(17):1573-619.
  4. Recent cancer survival in Europe: a 2000-02 period analysis of EUROCARE-4 data. Lancet Oncol 2007;8:784-96
  5. Peacock, AJ et al. An Epidemiological study of pulmonary arterial hypertension. EurRespir J 2007;30:527-41